Congenital Desmoid Fibroma of the Soft Tissues in a 6-Month-Old Girl

A desmoid tumor (DT), also known as aggressive fibromatosis, is a benign neoplasia of the soft tissues. It arises from conjonctive tissues, fascial sheaths, and muscular aponeurotic structures of muscles. According to biological characteristics, they are classified into three groups: -sporadic, -associated with familial adenomatous polyposis, -and familial or multicentric form. The pediatric form is ranged as a fourth group. To our knowledge, we report the first case in the world of congenital desmoid fibroma in the soft tissues of the ankle in a 6-month-old girl who is treated by surgical resection, with a good evolution over a 6-year follow-up. Through this observation, the authors suggest a review of the literature.